Cystic fibrosis (CF)
- CFTR modulator therapy is genotype-specific and transformative
- Airway clearance remains foundational
- Inhaled antibiotics treat chronic selected airway infection
- Dornase alfa/hypertonic saline improve mucus clearance
- Pancreatic enzymes + nutrition treat malabsorption
- Manage pulmonary exacerbations aggressively
Use at a glance
- CFTR modulator therapy is genotype-specific and transformative
Practical pearls
- Airway clearance remains foundational
Other practical pearls
- Dornase alfa/hypertonic saline improve mucus clearance
- Pancreatic enzymes + nutrition treat malabsorption
Choosing treatment
- Inhaled antibiotics treat chronic selected airway infection
- Manage pulmonary exacerbations aggressively
Self-check
- What determines selection of CFTR modulator therapy in Cystic fibrosis (CF)?
Genotype.
Drugs used for this (3)
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