Idiopathic pulmonary fibrosis (IPF)
- Confirm diagnosis with ILD expertise
- Antifibrotic therapy slows FVC decline
- nintedanib, pirfenidone, nerandomilast
- Treat hypoxemia, reflux symptoms + comorbidity
- Pulmonary rehab improves function
- Avoid chronic immunosuppression for idiopathic IPF
- Refer early for transplant when appropriate
Use at a glance
- Confirm diagnosis with ILD expertise
Treatment options
- Antifibrotic therapy slows FVC decline
- nintedanib, pirfenidone, nerandomilast
- Pulmonary rehab improves function
Escalation / refractory disease
- Treat hypoxemia, reflux symptoms + comorbidity
- Refer early for transplant when appropriate
Safety / pitfalls
- Avoid chronic immunosuppression for idiopathic IPF
Self-check
- What does antifibrotic therapy do to FVC decline in IPF?
Slows it. - Which chronic therapy is avoided in IPF?
Immunosuppression.
Drugs used for this (3)
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