Chronic thromboembolic pulmonary hypertension (CTEPH)
- Lifelong anticoagulation is generally required
- Pulmonary endarterectomy is potentially curative
- Balloon pulmonary angioplasty for selected inoperable disease
- Riociguat treats inoperable/persistent CTEPH
- Refer to an expert CTEPH center
- Do not manage as generic PAH without operability review
Use at a glance
- Lifelong anticoagulation is generally required
Practical pearls
- Pulmonary endarterectomy is potentially curative
- Riociguat treats inoperable/persistent CTEPH
- Refer to an expert CTEPH center
Choosing treatment
- Balloon pulmonary angioplasty for selected inoperable disease
Safety / pitfalls
- Do not manage as generic PAH without operability review
Self-check
- What is generally required lifelong in CTEPH?
Anticoagulation. - Which CTEPH procedure is potentially curative?
Pulmonary endarterectomy.
Drugs used for this (1)
All clinical uses · Open Chronic thromboembolic pulmonary hypertension (CTEPH) in the interactive console ↗